Rapid-onset dystonia-parkinsonism

Handb Clin Neurol. 2011:100:559-62. doi: 10.1016/B978-0-444-52014-2.00040-9.

Abstract

Rapid-onset dystonia-parkinsonism (RDP) is a rare condition with autosomal-dominant inheritance causing dystonia and parkinsonism which develop over a short period of time. It results from abnormalities in the Na(+)/K(+)-ATPase pump due to mutations in the ATP1A3 gene. This chapter reviews the clinical features, genetics, and diagnosis of this disorder.

Publication types

  • Review

MeSH terms

  • Diagnosis, Differential
  • Dystonic Disorders* / diagnosis
  • Dystonic Disorders* / genetics
  • Dystonic Disorders* / therapy
  • Humans

Supplementary concepts

  • Dystonia 12