Abstract
Interstitial lung diseases (ILDs) may be complicated by the development of pulmonary hypertension (PH), which is associated with worse functional impairment and a poorer prognosis. This article reviews the current state of knowledge on the prevalence, pathogenesis, diagnosis and prognosis of ILD-related PH. Whether the treatment of ILD-related PH changes clinical outcomes is currently unknown, but the current studies are summarized and the authors' perspective is offered.
MeSH terms
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Antihypertensive Agents / therapeutic use
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Blood Pressure
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Humans
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Hypertension, Pulmonary / diagnosis
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Hypertension, Pulmonary / drug therapy
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Hypertension, Pulmonary / epidemiology
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Hypertension, Pulmonary / etiology*
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Hypertension, Pulmonary / physiopathology
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Lung Diseases, Interstitial / complications*
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Lung Diseases, Interstitial / diagnosis
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Lung Diseases, Interstitial / drug therapy
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Lung Diseases, Interstitial / epidemiology
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Lung Diseases, Interstitial / physiopathology
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Treatment Outcome