Access to the complement factor B scissile bond is facilitated by association of factor B with C3b protein

J Biol Chem. 2011 Oct 14;286(41):35725-35732. doi: 10.1074/jbc.M111.263418. Epub 2011 Aug 23.

Abstract

Factor B is a zymogen that carries the catalytic site of the complement alternative pathway C3 convertase. During convertase assembly, factor B associates with C3b and Mg(2+) forming a pro-convertase C3bB(Mg(2+)) that is cleaved at a single factor B site by factor D. In free factor B, a pair of salt bridges binds the Arg(234) side chain to Glu(446) and to Glu(207), forming a double latch structure that sequesters the scissile bond (between Arg(234) and Lys(235)) and minimizes its unproductive cleavage. It is unknown how the double latch is released in the pro-convertase. Here, we introduce single amino acid substitutions into factor B that preclude one or both of the Arg(234) salt bridges, and we examine their impact on several different pro-convertase complexes. Our results indicate that loss of the Arg(234)-Glu(446) salt bridge partially stabilizes C3bB(Mg(2+)). Loss of the Arg(234)-Glu(207) salt bridge has lesser effects. We propose that when factor B first associates with C3b, it bears two intact Arg(234) salt bridges. The complex rapidly dissociates unless the Arg(234)-Glu(446) salt bridge is released whereupon conformational changes occur that activate the metal ion-dependent adhesion site and partially stabilize the complex. The remaining salt bridge is then released, exposing the scissile bond and permitting factor D cleavage.

Publication types

  • Research Support, N.I.H., Extramural

MeSH terms

  • Amino Acid Substitution
  • Complement C3b / chemistry*
  • Complement C3b / genetics
  • Complement C3b / metabolism
  • Complement Factor B / chemistry*
  • Complement Factor B / genetics
  • Complement Factor B / metabolism
  • Complement Factor D / chemistry*
  • Complement Factor D / genetics
  • Complement Factor D / metabolism
  • Humans
  • Multienzyme Complexes / chemistry*
  • Multienzyme Complexes / genetics
  • Multienzyme Complexes / metabolism
  • Mutation, Missense
  • Protein Binding

Substances

  • Multienzyme Complexes
  • Complement C3b
  • Complement Factor D
  • Complement Factor B