Expansion of neurofilament medium C terminus increases axonal diameter independent of increases in conduction velocity or myelin thickness

J Neurosci. 2012 May 2;32(18):6209-19. doi: 10.1523/JNEUROSCI.0647-12.2012.

Abstract

Maturation of the peripheral nervous system requires specification of axonal diameter, which, in turn, has a significant influence on nerve conduction velocity. Radial axonal growth initiates with myelination, and is dependent upon the C terminus of neurofilament medium (NF-M). Molecular phylogenetic analysis in mammals suggested that expanded NF-M C termini correlated with larger-diameter axons. We used gene targeting and computational modeling to test this new hypothesis. Increasing the length of NF-M C terminus in mice increased diameter of motor axons without altering neurofilament subunit stoichiometry. Computational modeling predicted that an expanded NF-M C terminus extended farther from the neurofilament core independent of lysine-serine-proline (KSP) phosphorylation. However, expansion of NF-M C terminus did not affect the distance between adjacent neurofilaments. Increased axonal diameter did not increase conduction velocity, possibly due to a failure to increase myelin thickness by the same proportion. Failure of myelin to compensate for larger axonal diameters suggested a lack of plasticity during the processes of myelination and radial axonal growth.

Publication types

  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't
  • Research Support, U.S. Gov't, Non-P.H.S.

MeSH terms

  • Animals
  • Axons / physiology*
  • Axons / ultrastructure*
  • Cells, Cultured
  • Mice
  • Mice, Transgenic
  • Myelin Sheath / metabolism*
  • Myelin Sheath / ultrastructure*
  • Neural Conduction / physiology*
  • Neurofilament Proteins / metabolism*
  • Neurofilament Proteins / ultrastructure*
  • Protein Conformation

Substances

  • Neurofilament Proteins
  • neurofilament protein M