A porcine model of familial adenomatous polyposis

Gastroenterology. 2012 Nov;143(5):1173-1175.e7. doi: 10.1053/j.gastro.2012.07.110. Epub 2012 Aug 1.

Abstract

We created gene-targeted pigs with mutations in the adenomatous polyposis coli (APC) gene (APC) that are orthologous to those responsible for human familial adenomatous polyposis (FAP). One-year-old pigs with the APC(1311) mutation (orthologous to human APC(1309)) have aberrant crypt foci and low- and high-grade dysplastic adenomas in the large intestine, similar to the precancerous lesions that develop in patients with FAP. Dysplastic adenomas accumulate β-catenin and lose heterozygosity of APC. This large-animal, genetic model of FAP will be useful in the development of diagnostics and therapeutics for colorectal cancer. DNA sequence data: NCBI accession number GU951771.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adenomatous Polyposis Coli / genetics*
  • Adenomatous Polyposis Coli / metabolism
  • Adenomatous Polyposis Coli / pathology*
  • Animals
  • Disease Models, Animal*
  • Genes, APC*
  • Heterozygote
  • Humans
  • Male
  • Mutation
  • Swine
  • beta Catenin / metabolism

Substances

  • beta Catenin