Insertional translocation of 15q25-q26 into 11p13 and duplication at 8p23.1 characterized by high resolution arrays in a boy with congenital malformations and aniridia

Am J Med Genet A. 2012 Nov;158A(11):2905-10. doi: 10.1002/ajmg.a.35603. Epub 2012 Sep 18.

Abstract

We report on a boy presenting submucous cleft palate, hydronephrosis, ventriculoseptal defect, aniridia, and developmental delay. Additional material on 11p13 was cytogenetically visible and array analyses identified a duplicated segment on 15q25-26 chromosome region; further, array analyses revealed a small deletion (49 kb) at 11p13 region involving the ELP4 gene and a duplication at 8p23.1. Results were confirmed with both molecular and molecular cytogenetics techniques. Possibilities for etiological basis of clinical phenotype are discussed.

Publication types

  • Case Reports
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Abnormalities, Multiple / diagnosis
  • Abnormalities, Multiple / genetics*
  • Aniridia / diagnosis
  • Aniridia / genetics*
  • Child, Preschool
  • Chromosomes, Human, Pair 11*
  • Chromosomes, Human, Pair 15*
  • Chromosomes, Human, Pair 8
  • Comparative Genomic Hybridization
  • Humans
  • In Situ Hybridization, Fluorescence
  • Karyotype
  • Male
  • Phenotype
  • Translocation, Genetic*
  • Trisomy*

Supplementary concepts

  • Chromosome 8, trisomy