RNAi screening identifies mediators of NOD2 signaling: implications for spatial specificity of MDP recognition

Proc Natl Acad Sci U S A. 2012 Dec 26;109(52):21426-31. doi: 10.1073/pnas.1209673109. Epub 2012 Dec 3.

Abstract

The intracellular nucleotide-binding oligomerization domain-2 (NOD2) receptor detects bacteria-derived muramyl dipeptide (MDP) and activates the transcription factor NF-κB. Here we describe the regulatome of NOD2 signaling using a systematic RNAi screen. Using three consecutive screens, we identified a set of 20 positive NF-κB regulators including the known pathway members RIPK2, RELA, and BIRC4 (XIAP) as well as FRMPD2 (FERM and PDZ domain-containing 2). FRMPD2 interacts with NOD2 via leucine-rich repeats and forms a complex with the membrane-associated protein ERBB2IP. We demonstrate that FRMPD2 spatially assembles the NOD2-signaling complex, hereby restricting NOD2-mediated immune responses to the basolateral compartment of polarized intestinal epithelial cells. We show that genetic truncation of the NOD2 leucine-rich repeat domain, which is associated with Crohn disease, impairs the interaction with FRMPD2, and that intestinal inflammation leads to down-regulation of FRMPD2. These results suggest a structural mechanism for how polarity of epithelial cells acts on intestinal NOD-like receptor signaling to mediate spatial specificity of bacterial recognition and control of immune responses.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Acetylmuramyl-Alanyl-Isoglutamine / metabolism*
  • Acetylmuramyl-Alanyl-Isoglutamine / pharmacology
  • Caco-2 Cells
  • Cell Membrane / drug effects
  • Cell Membrane / metabolism
  • Crohn Disease / metabolism
  • Crohn Disease / pathology
  • Enterocytes / drug effects
  • Enterocytes / metabolism
  • HEK293 Cells
  • Humans
  • Models, Biological
  • Mutant Proteins / metabolism
  • NF-kappa B / metabolism
  • Nod2 Signaling Adaptor Protein / chemistry
  • Nod2 Signaling Adaptor Protein / metabolism*
  • Protein Binding / drug effects
  • Protein Structure, Tertiary
  • RNA Interference*
  • RNA, Small Interfering / metabolism
  • Receptor-Interacting Protein Serine-Threonine Kinase 2 / metabolism
  • Reproducibility of Results
  • Signal Transduction* / drug effects
  • Substrate Specificity / drug effects
  • Tight Junction Proteins / chemistry

Substances

  • FRMPD2 protein, human
  • Mutant Proteins
  • NF-kappa B
  • Nod2 Signaling Adaptor Protein
  • RNA, Small Interfering
  • Tight Junction Proteins
  • Acetylmuramyl-Alanyl-Isoglutamine
  • Receptor-Interacting Protein Serine-Threonine Kinase 2