Postpneumococcal Moyamoya syndrome case report and review of the postinfective cases

BMJ Case Rep. 2013 Feb 6:2013:bcr2012006726. doi: 10.1136/bcr-2012-006726.

Abstract

Our aim was to describe a patient who experienced a postpneumococcal Moyamoya syndrome (MMS), with a great involvement of the posterior cerebral circulation, and to review the MMS postinfective cases. A 55-year-old Pakistani man with a history of pneumococcal meningitis 3 months before developed acute headache, left otalgia and body paresthesiae. Brain CT showed a right occipital ischaemic lesion. Seven days later, he developed acute left haemianopsia, haemiplegia, haemineglect and 'frontal' cognitive and behavioural symptoms. A second brain CT and MRI disclosed an increase in the occipital lesion and the appearance of a further one in the right frontal lobe. Cerebral CT and MRI-angiography were consistent with Moyamoya vessel alterations. Treatment with antiplatelets, methylprednisolone, followed by prednisone tapering, and motor rehabilitation began. Six months later, no relapses had occurred. Our case represents a delayed manifestation of postmeningitis vasculopathy. Meningitis may represent a risk factor for developing a disabling cerebrovascular disease like MMS.

Publication types

  • Case Reports
  • Review

MeSH terms

  • Cerebral Angiography
  • Humans
  • Male
  • Meningitis, Pneumococcal / complications*
  • Middle Aged
  • Moyamoya Disease / complications
  • Moyamoya Disease / diagnostic imaging*
  • Risk Factors
  • Time Factors