Localization of function-specific segments of the primary motor pathway in children with Sturge-Weber syndrome: a multimodal imaging analysis

J Magn Reson Imaging. 2013 Nov;38(5):1152-61. doi: 10.1002/jmri.24076. Epub 2013 Mar 5.

Abstract

Purpose: To explore whether diffusion-weighted imaging (DWI) can localize specific segments of primary motor areas in children with Sturge-Weber syndrome (SWS), this study investigated the corticospinal tract (CST) between precentral gyrus (PCG) and posterior limb of internal capsule (PIC).

Materials and methods: DWI was performed on 32 healthy children and seven children with unilateral SWS affecting the sensorimotor area variably. A hierarchical dendrogram was applied to find PCG-segments uniquely connected to PIC-segments. The resulting PCG-clusters were used to image primary motor pathways in DWI and find metabolic abnormalities of primary motor areas in positron emission tomography (PET) scans.

Results: In healthy children, five PCG-clusters were found to have unique CST courses, corresponding to CST segments of mouth/lip, fingers, and leg/ankle primary motor areas determined by functional magnetic resonance imaging (fMRI). In children with SWS, reduced streamlines in these PCG clusters were highly correlated with glucose-hypometabolism on PET (R(2) = 0.2312, P = 0.0032). Impaired CST segment corresponding to finger movements correlated with severity of hand motor deficit.

Conclusion: The presented method can detect impaired CST segments corresponding to specific motor functions in young children who cannot cooperate for fMRI. This approach can be clinically useful for a noninvasive presurgical evaluation of cortical motor areas in such children.

Keywords: Sturge-Weber syndrome; cortico-spinal tract; diffusion weighted imaging tractography; multimodal analysis; primary motor areas.

Publication types

  • Research Support, N.I.H., Extramural

MeSH terms

  • Child
  • Connectome / methods*
  • Diffusion Tensor Imaging / methods
  • Efferent Pathways / pathology*
  • Female
  • Fluorodeoxyglucose F18
  • Humans
  • Male
  • Motor Cortex / pathology*
  • Multimodal Imaging / methods*
  • Positron-Emission Tomography / methods
  • Radiopharmaceuticals
  • Reproducibility of Results
  • Sensitivity and Specificity
  • Somatosensory Cortex / pathology*
  • Sturge-Weber Syndrome / pathology*

Substances

  • Radiopharmaceuticals
  • Fluorodeoxyglucose F18