Issues in pediatric haemophilia care

Ital J Pediatr. 2013 Apr 20:39:24. doi: 10.1186/1824-7288-39-24.

Abstract

The hemophilias are the most common X-linked inherited bleeding disorders. The challenges in children are different from that in adults and, If not properly managed, can lead to chronic disease and lifelong disabilities. Currently, inhibitors are the most severe complication and prophylaxis is emerging as the optimal preventive care strategy. Quality of life has become in the western countries the primary objective of the process of providing care, thus all the strategies (psychotherapy, physiotherapy, community life), not just the infusion of the missing factor, should be activated for the patient and family to give them the perception of being healthy.

Publication types

  • Review

MeSH terms

  • Child
  • Coagulants / administration & dosage*
  • Delivery of Health Care / organization & administration
  • Evidence-Based Medicine
  • Factor IX / administration & dosage*
  • Factor VIII / administration & dosage*
  • Hemophilia A / diagnosis
  • Hemophilia A / drug therapy*
  • Hemophilia A / epidemiology
  • Hemophilia A / prevention & control
  • Hemophilia B / diagnosis
  • Hemophilia B / drug therapy*
  • Hemophilia B / epidemiology
  • Hemophilia B / prevention & control
  • Humans
  • Italy / epidemiology
  • Musculoskeletal Diseases / prevention & control
  • Quality of Life*
  • Risk Factors
  • Social Support
  • Treatment Outcome

Substances

  • Coagulants
  • Factor VIII
  • Factor IX