Intrinsic molecular factors cause aberrant expansion of the splenic marginal zone B cell population in nonobese diabetic mice

J Immunol. 2013 Jul 1;191(1):97-109. doi: 10.4049/jimmunol.1203252. Epub 2013 Jun 5.

Abstract

Marginal zone (MZ) B cells are an innate-like population that oscillates between MZ and follicular areas of the splenic white pulp. Differentiation of B cells into the MZ subset is governed by BCR signal strength and specificity, NF-κB activation through the B cell-activating factor belonging to the TNF family (BAFF) receptor, Notch2 signaling, and migration signals mediated by chemokine, integrin, and sphingosine-1-phosphate receptors. An imbalance in splenic B cell development resulting in expansion of the MZ subset has been associated with autoimmune pathogenesis in various murine models. One example is the NOD inbred mouse strain, in which MZ B cell expansion has been linked to development of type 1 diabetes and Sjögren's syndrome. However, the cause of MZ B cell expansion in this strain remains poorly understood. We have determined that increased MZ B cell development in NOD mice is independent of T cell autoimmunity, BCR specificity, BCR signal strength, and increased exposure to BAFF. Rather, mixed bone marrow chimeras showed that the factor(s) responsible for expansion of the NOD MZ subset is B cell intrinsic. Analysis of microarray expression data indicated that NOD MZ and precursor transitional 2-MZ subsets were particularly dysregulated for genes controlling cellular trafficking, including Apoe, Ccbp2, Cxcr7, Lgals1, Pla2g7, Rgs13, S1pr3, Spn, Bid, Cd55, Prf1, and Tlr3. Furthermore, these B cell subsets exhibited an increased steady state dwell time within splenic MZ areas. Our data therefore reveal that precursors of mature B cells in NOD mice exhibit an altered migration set point, allowing increased occupation of the MZ, a niche favoring MZ B cell differentiation.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Animals
  • B-Cell Activating Factor / deficiency
  • B-Cell Activating Factor / physiology*
  • B-Cell Activation Factor Receptor / physiology
  • B-Lymphocyte Subsets / immunology*
  • B-Lymphocyte Subsets / metabolism
  • B-Lymphocyte Subsets / pathology
  • Cell Differentiation / genetics
  • Cell Differentiation / immunology*
  • Female
  • Humans
  • Male
  • Mice
  • Mice, Inbred BALB C
  • Mice, Inbred C57BL
  • Mice, Inbred DBA
  • Mice, Inbred NOD
  • Mice, Transgenic
  • Proprotein Convertases / physiology
  • Receptor, Notch2 / physiology*
  • Receptors, Antigen, B-Cell / physiology*
  • Receptors, Lysosphingolipid / physiology*
  • Serine Endopeptidases / physiology
  • Spleen / immunology*
  • Spleen / metabolism
  • Spleen / pathology

Substances

  • B-Cell Activating Factor
  • B-Cell Activation Factor Receptor
  • Notch2 protein, mouse
  • Receptor, Notch2
  • Receptors, Antigen, B-Cell
  • Receptors, Lysosphingolipid
  • Tnfrsf13c protein, mouse
  • Tnfsf13b protein, mouse
  • Proprotein Convertases
  • Serine Endopeptidases
  • membrane-bound transcription factor peptidase, site 1