Introduction: fetal rhabdomyoma is the most common fetal cardiac tumor and is often associated with tuberous sclerosis. Usually the tumors are relatively small and show no mediastinal shift. Fetal hydrops and pericardial effusion are rarely seen.
Case: in this case report we present the neonatal clinical course of a case of prenatal diagnosis of giant cardiac rhabdomyomas.
Conclusion: an early prenatal diagnosis may help for an adequate planning of perinatal monitoring and treatment with involvement of a multidisciplinary team.
Keywords: fetal cardiac tumor; rhabdomyoma; tuberous sclerosis.