Allelic-dependent expression of an activating Fc receptor on B cells enhances humoral immune responses

Sci Transl Med. 2013 Dec 18;5(216):216ra175. doi: 10.1126/scitranslmed.3007097.

Abstract

B cells are pivotal regulators of acquired immune responses, and recent work in both experimental murine models and humans has demonstrated that subtle changes in the regulation of B cell function can substantially alter immunological responses. The balance of negative and positive signals in maintaining an appropriate B cell activation threshold is critical in B lymphocyte immune tolerance and autoreactivity. FcγRIIb (CD32B), the only recognized Fcγ receptor on B cells, provides immunoglobulin G (IgG)-mediated negative modulation through a tyrosine-based inhibition motif, which down-regulates B cell receptor-initiated signaling. These properties make FcγRIIb a promising target for antibody-based therapy. We report the discovery of allele-dependent expression of the activating FcγRIIc on B cells. Identical to FcγRIIb in the extracellular domain, FcγRIIc has a tyrosine-based activation motif in its cytoplasmic domain. In both human B cells and B cells from mice transgenic for human FcγRIIc, FcγRIIc expression counterbalances the negative feedback of FcγRIIb and enhances humoral responses to immunization in mice and to BioThrax vaccination in a human anthrax vaccine trial. Moreover, the FCGR2C-ORF allele is associated with the risk of development of autoimmunity in humans. FcγRIIc expression on B cells challenges the prevailing paradigm of unidirectional negative feedback by IgG immune complexes via the inhibitory FcγRIIb, is a previously unrecognized determinant in human antibody/autoantibody responses, and opens the opportunity for more precise personalized use of B cell-targeted antibody-based therapy.

Publication types

  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adult
  • Alleles
  • Animals
  • Anthrax Vaccines / administration & dosage
  • Autoimmunity / genetics
  • B-Lymphocytes / immunology*
  • Base Sequence
  • Cell Line
  • Codon, Terminator / genetics
  • Female
  • Gene Expression
  • Homozygote
  • Humans
  • Immunity, Humoral
  • Male
  • Mice
  • Mice, Transgenic
  • Middle Aged
  • Open Reading Frames
  • Polymorphism, Single Nucleotide
  • Protein Structure, Tertiary
  • Receptors, Antigen, B-Cell / metabolism
  • Receptors, IgG / chemistry
  • Receptors, IgG / genetics*
  • Receptors, IgG / metabolism*
  • Signal Transduction
  • Translational Research, Biomedical

Substances

  • Anthrax Vaccines
  • Codon, Terminator
  • FCGR2B protein, human
  • Fc gamma receptor IIC
  • Receptors, Antigen, B-Cell
  • Receptors, IgG