Hemangiopericytoma of the parapharyngeal space: a diagnostic challenge

ORL J Otorhinolaryngol Relat Spec. 2014;76(2):76-80. doi: 10.1159/000360480. Epub 2014 Apr 23.

Abstract

Parapharyngeal space tumors are known for having a difficult approach, misleading diagnosis and for representing a treatment challenge. Hemangiopericytomas account for less than 1% of all vascular neoplasms and 3% of all soft tissue sarcomas. Only 14 cases have been reported in the worldwide literature in this location. We present a case of a 44-year-old male who was referred for evaluation. A CT scan and MRI showed a large parapharyngeal mass of a possible salivary gland origin. The patient underwent a lateral cervicotomy associated with a transparotid-transmandibular approach, obtaining a vimentin-positive immunostaining tumor defining the diagnosis. The accurate management and prognosis of this type of neoplasm are provided by the definite diagnosis obtained by a correct histopathologic assessment. A high clinical suspicion is essential.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Hemangiopericytoma / diagnosis*
  • Hemangiopericytoma / metabolism
  • Hemangiopericytoma / pathology
  • Hemangiopericytoma / surgery
  • Humans
  • Immunohistochemistry
  • Magnetic Resonance Imaging
  • Male
  • Pharyngeal Neoplasms / diagnosis
  • Pharyngeal Neoplasms / metabolism
  • Pharyngeal Neoplasms / pathology
  • Pharyngeal Neoplasms / surgery
  • Prognosis
  • Tomography, X-Ray Computed