Tissue studies in screened first-degree relatives reveal a distinct Crohn's disease phenotype

Inflamm Bowel Dis. 2014 Jun;20(6):1049-56. doi: 10.1097/MIB.0000000000000051.

Abstract

Background: First-degree relatives of patients with Crohn's disease (CD) are at risk of developing the disease with 5% to 15% reported to be affected over time. Yet, a much greater proportion of them (>40%) shows features of "subclinical inflammation" with elevated intestinal inflammatory markers such as fecal calprotectin. The meaning of these findings is unclear in the absence of tissue data.

Methods: Thirty-eight asymptomatic first-degree relatives of patients with CD underwent ileocolonoscopy and other tests including fecal calprotectin. All known causes of intestinal inflammation were carefully excluded. Age and gender-matched controls consisted of 10 individuals who underwent colonoscopy for other reasons. Histology was scored based on known methods.

Results: Compared with controls, the relatives had significantly greater median values for fecal calprotectin and histological scores. In relatives, endoscopy identified 3 different phenotypes: (1) normal, (2) with minor lesions (aphthae or small superficial erosions), and (3) with typical CD inflammation. Based on the histological scores, the clustering analysis produced 3 corresponding highly separated clusters (61%, 26%, and 13% of the total, respectively) with divisive coefficient D = 0.94. When followed up (on the average for 53 mo), individuals in the second cluster had histological scores similar to baseline values (P = 0.12).

Conclusions: Tissue studies in first-degree relatives of patients with CD reveal 3 distinct groups: normal, with minimal inflammation, and with frank disease. The second cluster represents a novel phenotype, which does not seem to develop the disease over time. These findings explain previous observations of "subclinical inflammation" in such population.

MeSH terms

  • Adult
  • Biomarkers / metabolism
  • Colon / immunology
  • Colon / pathology
  • Colonoscopy
  • Crohn Disease / epidemiology*
  • Crohn Disease / genetics*
  • Crohn Disease / pathology
  • Endoscopy, Gastrointestinal
  • Family
  • Feces / chemistry
  • Female
  • Genetic Predisposition to Disease / epidemiology
  • Genetic Predisposition to Disease / genetics
  • Genetic Testing
  • Humans
  • Ileum / immunology
  • Ileum / pathology
  • Intestinal Absorption / immunology
  • Leukocyte L1 Antigen Complex / analysis
  • Male
  • Middle Aged
  • Phenotype
  • Risk Factors
  • Severity of Illness Index

Substances

  • Biomarkers
  • Leukocyte L1 Antigen Complex