Chest wall reconstruction in Marfan syndrome following aortic root replacement

Asian Cardiovasc Thorac Ann. 2014 Sep;22(7):872-4. doi: 10.1177/0218492313496586. Epub 2013 Oct 25.

Abstract

Chest wall and spine deformities are common in Marfan syndrome, and often coexist with cardiac defects. Surgery is often needed to both the aortic root and the anterior chest wall, and early spinal surgery is not uncommon. We describe a case of severe thoracic cage deformity with aortic root dilatation, which was managed by a staged approach, with a very good final result.

Keywords: Aorta; Dilatation; Funnel chest; Marfan syndrome; pathologic; thoracic.

Publication types

  • Case Reports

MeSH terms

  • Adolescent
  • Aortic Aneurysm / diagnosis
  • Aortic Aneurysm / etiology
  • Aortic Aneurysm / surgery*
  • Blood Vessel Prosthesis Implantation*
  • Humans
  • Magnetic Resonance Imaging
  • Male
  • Marfan Syndrome / complications*
  • Marfan Syndrome / diagnosis
  • Osteotomy*
  • Pectus Carinatum / complications
  • Pectus Carinatum / diagnosis
  • Pectus Carinatum / surgery*
  • Plastic Surgery Procedures*
  • Thoracic Surgical Procedures*
  • Treatment Outcome