Treatment of patients with adult T cell leukemia/lymphoma with cord blood transplantation: a Japanese nationwide retrospective survey

Biol Blood Marrow Transplant. 2014 Dec;20(12):1968-74. doi: 10.1016/j.bbmt.2014.08.012. Epub 2014 Aug 27.

Abstract

Allogeneic bone marrow and peripheral blood stem cell transplantations are curative treatment modalities for adult T cell leukemia/lymphoma (ATLL) because of the intrinsic graft-versus-ATLL effect. However, limited information is available regarding whether cord blood transplantation (CBT) induces a curative graft-versus-ATLL effect against aggressive ATLL. To evaluate the effect of CBT against ATLL, we retrospectively analyzed data from 175 patients with ATLL who initially underwent single-unit CBT. The 2-year overall survival (OS) rate was 20.6% (95% confidence interval [CI], 13.8% to 27.4%). A multivariate analysis revealed that the development of graft-versus-host disease (GVHD) was a favorable prognostic factor for OS (hazard ratio, .10; 95% CI, .01 to .94; P = .044). Furthermore, the 2-year OS (42.7%; 95% CI, 28.1% to 56.6%) of patients with grade 1 to 2 acute GVHD was higher than that of patients without acute GVHD (24.2%; 95% CI, 11.2% to 39.8%; P = .048). However, the cumulative incidence of treatment-related mortality (TRM) was high (46.1%; 95% CI, 38.2% to 53.7%), and early death was particularly problematic. In conclusion, CBT cures patients with ATLL partly through a graft-versus-ATLL effect. However, novel interventions will be required, particularly in the early phase, to reduce TRM and optimize GVHD.

Keywords: Adult T cell leukemia/lymphoma (ATTL); Cord blood transplantation; Graft-versus-adult T cell leukemia/lymphoma.

Publication types

  • Clinical Trial
  • Multicenter Study
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Acute Disease
  • Adult
  • Aged
  • Allografts
  • Bone Marrow Transplantation*
  • Cord Blood Stem Cell Transplantation*
  • Disease-Free Survival
  • Female
  • Graft vs Host Disease / etiology
  • Graft vs Host Disease / mortality
  • Graft vs Host Disease / therapy
  • Graft vs Leukemia Effect
  • Humans
  • Japan / epidemiology
  • Leukemia-Lymphoma, Adult T-Cell* / mortality
  • Leukemia-Lymphoma, Adult T-Cell* / therapy
  • Male
  • Middle Aged
  • Peripheral Blood Stem Cell Transplantation*
  • Retrospective Studies
  • Survival Rate