C-terminal domain small phosphatase 1 and MAP kinase reciprocally control REST stability and neuronal differentiation

Proc Natl Acad Sci U S A. 2014 Sep 16;111(37):E3929-36. doi: 10.1073/pnas.1414770111. Epub 2014 Sep 2.

Abstract

The repressor element 1 (RE1) silencing transcription factor (REST) in stem cells represses hundreds of genes essential to neuronal function. During neurogenesis, REST is degraded in neural progenitors to promote subsequent elaboration of a mature neuronal phenotype. Prior studies indicate that part of the degradation mechanism involves phosphorylation of two sites in the C terminus of REST that require activity of beta-transducin repeat containing E3 ubiquitin protein ligase, βTrCP. We identify a proline-directed phosphorylation motif, at serines 861/864 upstream of these sites, which is a substrate for the peptidylprolyl cis/trans isomerase, Pin1, as well as the ERK1/2 kinases. Mutation at S861/864 stabilizes REST, as does inhibition of Pin1 activity. Interestingly, we find that C-terminal domain small phosphatase 1 (CTDSP1), which is recruited by REST to neuronal genes, is present in REST immunocomplexes, dephosphorylates S861/864, and stabilizes REST. Expression of a REST peptide containing S861/864 in neural progenitors inhibits terminal neuronal differentiation. Together with previous work indicating that both REST and CTDSP1 are expressed to high levels in stem cells and down-regulated during neurogenesis, our results suggest that CTDSP1 activity stabilizes REST in stem cells and that ERK-dependent phosphorylation combined with Pin1 activity promotes REST degradation in neural progenitors.

Publication types

  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Animals
  • Cell Differentiation*
  • Chickens
  • Chromatin / metabolism
  • Epidermal Growth Factor / metabolism
  • Extracellular Signal-Regulated MAP Kinases / metabolism*
  • Green Fluorescent Proteins / metabolism
  • HEK293 Cells
  • Humans
  • MAP Kinase Signaling System
  • Mice
  • Mutation / genetics
  • NIMA-Interacting Peptidylprolyl Isomerase
  • Neurons / cytology*
  • Neurons / metabolism*
  • Nuclear Proteins / metabolism*
  • PC12 Cells
  • Peptides / metabolism
  • Peptidylprolyl Isomerase / metabolism
  • Phosphoprotein Phosphatases / metabolism*
  • Phosphorylation
  • Phosphoserine / metabolism
  • Protein Binding
  • Protein Stability
  • Proteolysis
  • Rats
  • Repressor Proteins / metabolism*
  • beta-Transducin Repeat-Containing Proteins / metabolism
  • ras Proteins / metabolism

Substances

  • Chromatin
  • NIMA-Interacting Peptidylprolyl Isomerase
  • Nuclear Proteins
  • Peptides
  • RE1-silencing transcription factor
  • Repressor Proteins
  • beta-Transducin Repeat-Containing Proteins
  • Green Fluorescent Proteins
  • Phosphoserine
  • Epidermal Growth Factor
  • Extracellular Signal-Regulated MAP Kinases
  • CTDSP1 protein, human
  • Phosphoprotein Phosphatases
  • ras Proteins
  • PIN1 protein, human
  • Peptidylprolyl Isomerase
  • Pin1 protein, mouse