Cholesterol metabolite cholestane-3β,5α,6β-triol suppresses epileptic seizures by negative modulation of voltage-gated sodium channels

Steroids. 2015 Jun:98:166-72. doi: 10.1016/j.steroids.2014.12.025. Epub 2015 Jan 8.

Abstract

Imbalance of excitation and inhibition in neurons is implicated in the pathogenesis of epilepsy. Voltage-gated sodium channels, which play a vital role in regulating neuronal excitability, are one of the major targets for developing anti-epileptic drugs. Here we provide evidence that cholestane-3β,5α,6β-triol (triol), a major metabolic oxysterol of cholesterol, is an effective state-dependent negative sodium channels modulator. Triol reduced Na(+) current density in a concentration-dependent manner. 10 μM triol shifted steady-state/fast/slow inactivation curves of sodium channels toward the hyperpolarizing direction. Additionally, triol reduced voltage-gated sodium currents in a voltage- and frequency-dependent manner. In a kainic acid-induced seizures mouse model, triol (25 mg/kg) significantly increased the latency of seizure onset and attenuated seizure severity. Our findings provide novel insights for understanding the modulatory role of a small molecular oxysterol on voltage-gated sodium channels and suggest triol may represent a novel and promising candidate for epilepsy intervention.

Keywords: Cholestane-3β-5α-6β-triol; Epilepsy; Oxysterol; Voltage-gated sodium channels.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Animals
  • Anticonvulsants / chemistry
  • Anticonvulsants / pharmacology*
  • Cholestanols / chemistry
  • Cholestanols / pharmacology*
  • Cholesterol / chemistry
  • Cholesterol / metabolism
  • Disease Models, Animal
  • Dose-Response Relationship, Drug
  • Epilepsy / chemically induced
  • Epilepsy / drug therapy*
  • Epilepsy / metabolism
  • Excitatory Amino Acid Agonists / adverse effects
  • Excitatory Amino Acid Agonists / pharmacology
  • Kainic Acid / adverse effects
  • Kainic Acid / pharmacology
  • Mice
  • Voltage-Gated Sodium Channel Blockers / chemistry
  • Voltage-Gated Sodium Channel Blockers / pharmacology*
  • Voltage-Gated Sodium Channels / metabolism*

Substances

  • Anticonvulsants
  • Cholestanols
  • Excitatory Amino Acid Agonists
  • Voltage-Gated Sodium Channel Blockers
  • Voltage-Gated Sodium Channels
  • cholestane-3,5,6-triol
  • Cholesterol
  • Kainic Acid