Familial 7q11.23 duplication with variable phenotype

Am J Med Genet A. 2015 Nov;167A(11):2727-30. doi: 10.1002/ajmg.a.37226. Epub 2015 Jun 24.

Abstract

Chromosomal microdeletions and microduplications are known to cause variable clinical features ranging from apparently normal phenotype to intellectual disability, multiple congenital anomalies, and/or other variable clinical features. 7q11.23 region deletion is the cause for Williams-Beuren syndrome and duplication of same region 7q11.23 causes distinguishable clinical phenotype. Familial inheritance is known for both microdeletion and microduplication of 7q11.23 region. Here, we report a patient of paternally inherited 7q11.23 microduplication with developmental delay, macrocephaly, and structural brain malformations.

Keywords: 7q11.23 duplication; congenital heart disease; dsygenesis and hypoplasia corpus callosum; hypoplasia of left cerebellum; macrocephaly.

Publication types

  • Case Reports

MeSH terms

  • Chromosome Duplication / genetics*
  • Chromosomes, Human, Pair 7 / genetics*
  • Family
  • Female
  • Humans
  • Infant
  • Infant, Newborn
  • Magnetic Resonance Imaging
  • Male
  • Phenotype