Intestinal metaplasia of appendiceal endometriosis is not uncommon and may mimic appendiceal mucinous neoplasm

Pathol Res Pract. 2017 Jan;213(1):39-44. doi: 10.1016/j.prp.2016.10.011. Epub 2016 Oct 25.

Abstract

Endometriosis of the appendix can be an incidental finding or a cause of appendicitis, intussusception, perforation or retention mucocele. Intestinal metaplasia of appendiceal endometriosis may occur, which can lead to a misdiagnosis of low-grade appendiceal mucinous neoplasm. On a retrospective search of the pathology database from 2001 to 2015, we identified 78 appendiceal endometriosis cases and intestinal metaplasia was present in 10/78 (13%) cases. In most of the cases (90%), the foci of intestinal metaplasia were mainly localized close to the mucosa. Intestinal and endometrial hybrid glands were present in 9/10 (90%) cases. These cases were often associated with marked appendiceal distortion, luminal obliteration and mass formation, causing concern for a mucinous neoplasm clinically and pathologically. Our findings indicate that intestinal metaplasia in appendiceal endometriosis is not an uncommon phenomenon, which can be mistaken for a mucinous neoplasm. Endometriosis should be kept in mind when a diagnosis of appendiceal mucinous neoplasm is made, especially in a young woman with a clinical history of endometriosis.

Keywords: Appendix; Endometriosis; Intestinal metaplasia; Mucinous neoplasm.

MeSH terms

  • Adenocarcinoma, Mucinous / pathology*
  • Adult
  • Appendiceal Neoplasms / pathology*
  • Cecal Diseases / pathology*
  • Databases, Factual
  • Diagnosis, Differential
  • Endometriosis / pathology*
  • Female
  • Humans
  • Intestines / pathology*
  • Metaplasia / pathology
  • Middle Aged
  • Retrospective Studies
  • Young Adult