The emerging role of interleukin (IL)-1 in the pathogenesis and treatment of inflammatory and degenerative eye diseases

Clin Rheumatol. 2017 Oct;36(10):2307-2318. doi: 10.1007/s10067-016-3527-z. Epub 2016 Dec 28.

Abstract

Interleukin (IL)-1 plays a key role in the pathogenesis and thereafter in the search for specific treatments of different inflammatory and degenerative eye diseases. Indeed, an overactivity of IL-1 might be an initiating factor for many immunopathologic sceneries in the eye, as proven by the efficacy of the specific IL-1 blockade in different ocular diseases. For instance, the uveitis in monogenic autoinflammatory disorders, such as Blau syndrome and cryopyrin-associated periodic syndrome, or in complex polygenic autoinflammatory disorders, such as Behçet's disease, has been successfully treated with IL-1 blockers. Similarly, therapy with the IL-1 receptor antagonist anakinra has proven successful also in scleritis and episcleritis in the context of different rheumatic conditions. Moreover, interesting findings deriving from animal models of ocular disease have set a rational basis from a therapeutic viewpoint to manage patients also with dry eye disease and a broadening number of ocular inflammatory and degenerative conditions, which start from an imbalance between IL-1 and its receptor antagonist.

Keywords: Diabetic retinopathy; Dry-eye; Keratitis; Macular degeneration; Scleritis; Uveitis.

Publication types

  • Review

MeSH terms

  • Animals
  • Disease Models, Animal
  • Dry Eye Syndromes / drug therapy
  • Dry Eye Syndromes / immunology
  • Eye Diseases / drug therapy*
  • Eye Diseases / immunology
  • Hereditary Autoinflammatory Diseases / drug therapy*
  • Hereditary Autoinflammatory Diseases / immunology
  • Humans
  • Inflammation / drug therapy*
  • Inflammation / immunology
  • Interleukin 1 Receptor Antagonist Protein / metabolism
  • Interleukin 1 Receptor Antagonist Protein / therapeutic use
  • Interleukin-1 / physiology*
  • Keratitis / drug therapy
  • Keratitis / immunology
  • Macular Degeneration / drug therapy
  • Macular Degeneration / immunology
  • NLR Family, Pyrin Domain-Containing 3 Protein / metabolism
  • Scleritis / drug therapy
  • Scleritis / immunology
  • Sjogren's Syndrome / drug therapy
  • Sjogren's Syndrome / immunology
  • Uveitis / drug therapy
  • Uveitis / immunology

Substances

  • IL1RN protein, human
  • Interleukin 1 Receptor Antagonist Protein
  • Interleukin-1
  • NLR Family, Pyrin Domain-Containing 3 Protein
  • NLRP3 protein, human