[Resection of a cardiac rhabdomyoma of the right and left ventricular outflow tract]

Z Kardiol. 1989 Sep;78(9):607-10.
[Article in German]

Abstract

Rhabdomyomas are benign cardiac tumors often occurring as multiple lesions. We describe an infant with multiple cardiac rhabdomyomas causing severe right-ventricular and left-ventricular outflow tract obstructions. The intracavitary parts of the rhabdomyomas were successfully resected when the patient was 5 weeks old. Echocardiography showed regression in size of the remaining intramural tumors. Since there is only a low growth potential in cardiac rhabdomyomas, surgical management is indicated only in patients with hemodynamic obstruction or significant arrhythmias. Surgery should be primarily directed to relieve hemodynamic obstruction. If complete resection is not possible without damage to vital structures, resection should be restricted to the intracavitary parts of the tumor.

Publication types

  • Case Reports
  • English Abstract

MeSH terms

  • Echocardiography
  • Heart Neoplasms / congenital*
  • Heart Neoplasms / surgery
  • Humans
  • Infant
  • Infant, Newborn
  • Male
  • Neoplasms, Multiple Primary / congenital*
  • Neoplasms, Multiple Primary / surgery
  • Rhabdomyoma / congenital*
  • Rhabdomyoma / surgery
  • Ventricular Outflow Obstruction / congenital*
  • Ventricular Outflow Obstruction / surgery