Sumoylation: Implications for Neurodegenerative Diseases

Adv Exp Med Biol. 2017:963:261-281. doi: 10.1007/978-3-319-50044-7_16.

Abstract

The covalent posttranslational modifications of proteins are critical events in signaling cascades that enable cells to efficiently, rapidly and reversibly respond to extracellular stimuli. This is especially important in the CNS where the processes affecting synaptic communication between neurons are highly complex and very tightly regulated. Sumoylation regulates the function and fate of a diverse array of proteins and participates in the complex cell signaling pathways required for cell survival. One of the most complex signaling pathways is synaptic transmission.Correct synaptic function is critical to the working of the brain and its alteration through synaptic plasticity mediates learning, mental disorders and stroke. The investigation of neuronal sumoylation is a new and exciting field and the functional and pathophysiological implications are far-reaching. Sumoylation has already been implicated in a diverse array of neurological disorders. Here we provide an overview of current literature highlighting recent insights into the role of sumoylation in neurodegeneration. In addition we present a brief assessment of drug discovery in the analogous ubiquitin system and extrapolate on the potential for development of novel therapies that might target SUMO-associated mechanisms of neurodegenerative disease.

Keywords: Alzheimer’s disease; Amyotrophic lateral sclerosis; Drug targets; Ischemia; Neuronal intranuclear inclusion disease; Parkinson’s disease; Polyglutamine diseases.

Publication types

  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't
  • Review

MeSH terms

  • Animals
  • Humans
  • Nerve Degeneration*
  • Neurodegenerative Diseases / drug therapy
  • Neurodegenerative Diseases / metabolism*
  • Neurodegenerative Diseases / pathology
  • Neurodegenerative Diseases / physiopathology
  • Neurons / drug effects
  • Neurons / metabolism*
  • Neurons / pathology
  • Neuroprotective Agents / therapeutic use
  • Signal Transduction* / drug effects
  • Small Ubiquitin-Related Modifier Proteins / metabolism*
  • Sumoylation*
  • Synaptic Transmission
  • Ubiquitin-Protein Ligases / metabolism*

Substances

  • Neuroprotective Agents
  • Small Ubiquitin-Related Modifier Proteins
  • Ubiquitin-Protein Ligases