1 *Department of Pathology †Department of Urology, European Georges Pompidou Hospital, APHP ‡Medical Faculty of Paris-Descartes University, Paris §PREDIR, National Expert Network of INCA for Rare Adult Cancers "Hereditary Predisposition to Renal Tumours", APHP, Bicetre Hospital, Le Kremlin-Bicêtre ∥INSERM U1186, Oncogenetic Laboratory, EPHE, PSL, Institut of Cancerology Gustave Roussy, Villejuif ¶Department of Pathology, Necker-Enfants Malades hospital, APHP, Paris **INSERM, UMR970, Paris-Centre de Recherche Cardiovasculaire, Paris, France.