Impact of Objective Echocardiographic Criteria for Timing of Congenital Diaphragmatic Hernia Repair

J Pediatr. 2018 Jan:192:99-104.e4. doi: 10.1016/j.jpeds.2017.09.004. Epub 2017 Nov 6.

Abstract

Objective: To assess the impact of specific echocardiographic criteria for timing of congenital diaphragmatic hernia repair on the incidence of acute postoperative clinical decompensation from pulmonary hypertensive crisis and/or acute respiratory decompensation, with secondary outcomes including survival to discharge, duration of ventilator support, and length of hospitalization.

Study design: The multidisciplinary congenital diaphragmatic hernia management team instituted a protocol in 2012 requiring the specific criterion of echocardiogram-estimated pulmonary artery pressure ≤80% systemic blood pressure before repairing congenital diaphragmatic hernias. A retrospective review of 77 neonatal patients with Bochdalek hernias repaired between 2008 and 2015 were reviewed: group 1 included patients repaired before protocol implementation (n = 25) and group 2 included patients repaired after implementation (n = 52).

Results: The groups had similar baseline characteristics. Postoperative decompensation occurred less often in group 2 compared with group 1 (17% vs 48%, P = .01). Adjusted analysis accounting for repair type, liver herniation, and prematurity yielded similar results (15% vs 37%, P = .04). Group 2 displayed a trend toward improved survival to 30 days postoperatively, though this did not reach statistical significance (94% vs 80%, P = .06). Patient survival to discharge, duration of ventilator support, and length of hospitalization were not different between groups.

Conclusions: The implementation of a protocol requiring echocardiogram-estimated pulmonary arterial pressure ≤80% of systemic pressure before congenital diaphragmatic hernia repair may reduce the incidence of acute postoperative decompensation, although there was no difference in longer-term secondary outcomes, including survival to discharge.

Keywords: congenital diaphragmatic hernias; operative therapy; pediatric surgery; surgical outcomes.

Publication types

  • Research Support, N.I.H., Extramural

MeSH terms

  • Arterial Pressure
  • Blood Pressure Determination
  • Clinical Decision-Making / methods*
  • Clinical Protocols
  • Echocardiography*
  • Female
  • Hernias, Diaphragmatic, Congenital / diagnostic imaging*
  • Hernias, Diaphragmatic, Congenital / physiopathology
  • Hernias, Diaphragmatic, Congenital / surgery
  • Herniorrhaphy*
  • Humans
  • Infant, Newborn
  • Length of Stay / statistics & numerical data
  • Logistic Models
  • Male
  • Postoperative Complications / epidemiology
  • Postoperative Complications / prevention & control
  • Preoperative Care / methods*
  • Retrospective Studies
  • Time Factors
  • Treatment Outcome