[Pedigree investigation and genetic analysis of a case with Vel heterozygous deletion mutation]

Zhonghua Yi Xue Yi Chuan Xue Za Zhi. 2017 Dec 10;34(6):888-890. doi: 10.3760/cma.j.issn.1003-9406.2017.06.023.
[Article in Chinese]

Abstract

Objective: To analyze an individual with SMIM1 c.64_80 heterozygous deletional mutation and his family members.

Methods: Based on the molecular basis of Vel negative blood type, PCR primers specific for SMIM1 wild-type allele and c.64_80del allele were designed. PCR-sequence specific primer (PCR-SSP) and Sanger sequencing were employed to determine the genotype of all subjects. Inheritance of the Vel blood group system was investigated by pedigree analysis.

Results: PCR-SSP and DNA sequencing demonstrated that the proband was heterozygous for the SMIM1 c.64_80del allele. Pedigree investigation showed that his father had the same mutation, while his mother and elder sister were of wide type. No individual with homozygous c.64_80del allele was found.

Conclusion: PCR-SSP and DNA sequencing confirmed that the proband was heterozygous for the c.64_80del mutation. The mutation inherits form his father.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Blood Group Antigens / genetics*
  • Female
  • Gene Deletion*
  • Genetic Testing
  • Homozygote
  • Humans
  • Male
  • Membrane Proteins / genetics*
  • Pedigree
  • Sequence Analysis, DNA

Substances

  • Blood Group Antigens
  • Membrane Proteins
  • SMIM1 protein, human