Integrated biology approach reveals molecular and pathological interactions among Alzheimer's Aβ42, Tau, TREM2, and TYROBP in Drosophila models

Genome Med. 2018 Mar 29;10(1):26. doi: 10.1186/s13073-018-0530-9.

Abstract

Background: Cerebral amyloidosis, neuroinflammation, and tauopathy are key features of Alzheimer's disease (AD), but interactions among these features remain poorly understood. Our previous multiscale molecular network models of AD revealed TYROBP as a key driver of an immune- and microglia-specific network that was robustly associated with AD pathophysiology. Recent genetic studies of AD further identified pathogenic mutations in both TREM2 and TYROBP.

Methods: In this study, we systematically examined molecular and pathological interactions among Aβ, tau, TREM2, and TYROBP by integrating signatures from transgenic Drosophila models of AD and transcriptome-wide gene co-expression networks from two human AD cohorts.

Results: Glial expression of TREM2/TYROBP exacerbated tau-mediated neurodegeneration and synergistically affected pathways underlying late-onset AD pathology, while neuronal Aβ42 and glial TREM2/TYROBP synergistically altered expression of the genes in synaptic function and immune modules in AD.

Conclusions: The comprehensive pathological and molecular data generated through this study strongly validate the causal role of TREM2/TYROBP in driving molecular networks in AD and AD-related phenotypes in flies.

Keywords: Alzheimer’s disease; Amyloid-β (Aβ) peptides; Differential expression; Gene co-expression network; Gene module; Immune function; Microtubule-associated protein tau; Neurodegeneration; Synaptophagy; TREM2 (triggering receptor expressed on myeloid cells 2); TYROBP (tyrosine kinase binding protein).

Publication types

  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adaptor Proteins, Signal Transducing / metabolism*
  • Alzheimer Disease / genetics*
  • Amyloid beta-Peptides / metabolism*
  • Animals
  • Animals, Genetically Modified
  • Brain / metabolism
  • Brain / pathology
  • Disease Models, Animal
  • Drosophila Proteins / genetics
  • Drosophila Proteins / metabolism*
  • Drosophila melanogaster / genetics*
  • Female
  • Gene Expression Regulation
  • Gene Regulatory Networks
  • Humans
  • Male
  • Membrane Glycoproteins / metabolism*
  • Membrane Proteins / metabolism*
  • Nerve Degeneration / genetics
  • Nerve Degeneration / pathology
  • Neuroglia / metabolism
  • Neurons / metabolism
  • Receptors, Immunologic / metabolism*
  • Signal Transduction / genetics
  • Synapses / metabolism
  • tau Proteins / metabolism*

Substances

  • Adaptor Proteins, Signal Transducing
  • Amyloid beta-Peptides
  • Drosophila Proteins
  • Membrane Glycoproteins
  • Membrane Proteins
  • Receptors, Immunologic
  • TREM2 protein, human
  • TYROBP protein, human
  • tau Proteins
  • tau protein, Drosophila