Primary Sjögren's syndrome

Lupus. 2018 Oct;27(1_suppl):32-35. doi: 10.1177/0961203318801673.

Abstract

Primary Sjögren's syndrome (pSS) is a systemic autoimmune disorder characterized by focal lymphocytic infiltration of the exocrine glands causing dry eyes and dry mouth. Similar glandular features can also occur as a late complication in patients with other rheumatic disorders, such as rheumatoid arthritis (RA), systemic lupus erythematosus (SLE) and scleroderma ('secondary' Sjögren's syndrome).1 Anti-Ro and/or anti-La (ENA) antibodies are found in approximately 70% of pSS patients, generally with ANA positivity. Hypergammaglobulinaemia is also common. Systemic features also occur in some patients with pSS. A positive rheumatoid factor (RF) is often seen and so if patients present with arthritis, dryness and a positive RF a diagnosis of pSS should be considered as a possible alternative to RA. Anti-CCP antibodies are more specific for RA.

Keywords: Dryness; Musculoskeletal; Sjögren’s syndrome; lymphoma.

Publication types

  • Review

MeSH terms

  • Antibodies, Antinuclear / blood
  • Arthritis, Rheumatoid / diagnosis
  • Humans
  • Hydroxychloroquine / therapeutic use
  • Hypergammaglobulinemia / diagnosis
  • Lupus Erythematosus, Systemic / diagnosis
  • Sjogren's Syndrome / diagnosis*
  • Sjogren's Syndrome / drug therapy

Substances

  • Antibodies, Antinuclear
  • Hydroxychloroquine