HRI coordinates translation necessary for protein homeostasis and mitochondrial function in erythropoiesis

Elife. 2019 Apr 29:8:e46976. doi: 10.7554/eLife.46976.

Abstract

Iron and heme play central roles in the production of red blood cells, but the underlying mechanisms remain incompletely understood. Heme-regulated eIF2α kinase (HRI) controls translation by phosphorylating eIF2α. Here, we investigate the global impact of iron, heme, and HRI on protein translation in vivo in murine primary erythroblasts using ribosome profiling. We validate the known role of HRI-mediated translational stimulation of integratedstressresponse mRNAs during iron deficiency in vivo. Moreover, we find that the translation of mRNAs encoding cytosolic and mitochondrial ribosomal proteins is substantially repressed by HRI during iron deficiency, causing a decrease in cytosolic and mitochondrial protein synthesis. The absence of HRI during iron deficiency elicits a prominent cytoplasmic unfolded protein response and impairs mitochondrial respiration. Importantly, ATF4 target genes are activated during iron deficiency to maintain mitochondrial function and to enable erythroid differentiation. We further identify GRB10 as a previously unappreciated regulator of terminal erythropoiesis.

Keywords: ATF4; cell biology; chromosomes; cytosolic and mitochondrial translation; erythropoiesis; gene expression; heme-regulated eIF2a kinase; integrated stress response; mitochondrial respiration; mouse.

Publication types

  • Research Support, N.I.H., Extramural

MeSH terms

  • Activating Transcription Factor 4 / genetics
  • Anemia, Iron-Deficiency
  • Animals
  • Cell Differentiation
  • Erythroblasts
  • Erythropoiesis / physiology*
  • Eukaryotic Initiation Factor-2 / metabolism
  • GRB10 Adaptor Protein / genetics
  • GRB10 Adaptor Protein / metabolism
  • Heme / metabolism*
  • Iron / metabolism*
  • Mice
  • Mice, Knockout
  • Mitochondria / metabolism*
  • Oxygen / metabolism
  • Phosphorylation
  • Protein Biosynthesis
  • Proteostasis / physiology*
  • Ribosomal Proteins
  • Unfolded Protein Response
  • eIF-2 Kinase / genetics
  • eIF-2 Kinase / metabolism*

Substances

  • Atf4 protein, mouse
  • Eukaryotic Initiation Factor-2
  • Grb10 protein, mouse
  • Ribosomal Proteins
  • Activating Transcription Factor 4
  • GRB10 Adaptor Protein
  • Heme
  • Iron
  • eIF-2 Kinase
  • Oxygen

Associated data

  • GEO/GSE119365