Tau tubulin kinases in proteinopathy

FEBS J. 2019 Jul;286(13):2434-2446. doi: 10.1111/febs.14866. Epub 2019 May 22.

Abstract

A number of neurodegenerative diseases are characterized by deposition of abnormally phosphorylated tau or TDP-43 in disease-affected neurons. These diseases include Alzheimer's disease, frontotemporal lobar degeneration, and amyotrophic lateral sclerosis. No disease-modifying therapeutics is available to treat these disorders, and we have a limited understanding of the cellular and molecular factors integral to disease initiation or progression. Phosphorylated tau and TDP-43 are important markers of pathology in dementia disorders and directly contribute to tau- and TDP-43-related neurotoxicity and neurodegeneration. Here, we review the scope of tau and TDP-43 phosphorylation in neurodegenerative disease and discuss recent work demonstrating the kinases TTBK1 and TTBK2 phosphorylate both tau and TDP-43, promoting neurodegeneration.

Keywords: ALS; CBD; FTLD; PSP; Alzheimer's disease; Pick's disease; TDP-43; TTBK1; TTBK2; phosphorylation; tau; tauopathy.

Publication types

  • Research Support, N.I.H., Extramural
  • Research Support, U.S. Gov't, Non-P.H.S.
  • Review

MeSH terms

  • Animals
  • Brain / metabolism
  • Brain / pathology
  • Humans
  • Protein Serine-Threonine Kinases / chemistry
  • Protein Serine-Threonine Kinases / genetics
  • Protein Serine-Threonine Kinases / metabolism*
  • TDP-43 Proteinopathies / metabolism*
  • TDP-43 Proteinopathies / pathology

Substances

  • tau-tubulin kinase
  • Protein Serine-Threonine Kinases