Immune homeostasis and regulation of the interferon pathway require myeloid-derived Regnase-3

J Exp Med. 2019 Jul 1;216(7):1700-1723. doi: 10.1084/jem.20181762. Epub 2019 May 24.

Abstract

The RNase Regnase-1 is a master RNA regulator in macrophages and T cells that degrades cellular and viral RNA upon NF-κB signaling. The roles of its family members, however, remain largely unknown. Here, we analyzed Regnase-3-deficient mice, which develop hypertrophic lymph nodes. We used various mice with immune cell-specific deletions of Regnase-3 to demonstrate that Regnase-3 acts specifically within myeloid cells. Regnase-3 deficiency systemically increased IFN signaling, which increased the proportion of immature B and innate immune cells, and suppressed follicle and germinal center formation. Expression analysis revealed that Regnase-3 and Regnase-1 share protein degradation pathways. Unlike Regnase-1, Regnase-3 expression is high specifically in macrophages and is transcriptionally controlled by IFN signaling. Although direct targets in macrophages remain unknown, Regnase-3 can bind, degrade, and regulate mRNAs, such as Zc3h12a (Regnase-1), in vitro. These data indicate that Regnase-3, like Regnase-1, is an RNase essential for immune homeostasis but has diverged as key regulator in the IFN pathway in macrophages.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • 3' Untranslated Regions
  • Animals
  • Autoimmunity
  • B-Lymphocytes / metabolism
  • Flow Cytometry
  • Gene Expression Regulation
  • Homeostasis / immunology*
  • Immunity, Innate*
  • Interferons / metabolism*
  • Macrophages / metabolism
  • Mice
  • Mice, Inbred C57BL
  • Mice, Knockout
  • Myeloid Cells / enzymology
  • Myeloid Cells / metabolism*
  • Real-Time Polymerase Chain Reaction
  • Ribonucleases / genetics
  • Ribonucleases / metabolism*
  • Signal Transduction
  • T-Lymphocytes / metabolism

Substances

  • 3' Untranslated Regions
  • Interferons
  • Ribonucleases
  • Zc3h12c protein, mouse