Early defects in translation elongation factor 1α levels at excitatory synapses in α-synucleinopathy

Acta Neuropathol. 2019 Dec;138(6):971-986. doi: 10.1007/s00401-019-02063-3. Epub 2019 Aug 26.

Abstract

Cognitive decline and dementia in neurodegenerative diseases are associated with synapse dysfunction and loss, which may precede neuron loss by several years. While misfolded and aggregated α-synuclein is recognized in the disease progression of synucleinopathies, the nature of glutamatergic synapse dysfunction and loss remains incompletely understood. Using fluorescence-activated synaptosome sorting (FASS), we enriched excitatory glutamatergic synaptosomes from mice overexpressing human alpha-synuclein (h-αS) and wild-type littermates to unprecedented purity. Subsequent label-free proteomic quantification revealed a set of proteins differentially expressed upon human alpha-synuclein overexpression. These include overrepresented proteins involved in the synaptic vesicle cycle, ER-Golgi trafficking, metabolism and cytoskeleton. Unexpectedly, we found and validated a steep reduction of eukaryotic translation elongation factor 1 alpha (eEF1A1) levels in excitatory synapses at early stages of h-αS mouse model pathology. While eEF1A1 reduction correlated with the loss of postsynapses, its immunoreactivity was found on both sides of excitatory synapses. Moreover, we observed a reduction in eEF1A1 immunoreactivity in the cingulate gyrus neuropil of patients with Lewy body disease along with a reduction in PSD95 levels. Altogether, our results suggest a link between structural impairments underlying cognitive decline in neurodegenerative disorders and local synaptic defects. eEF1A1 may therefore represent a limiting factor to synapse maintenance.

Keywords: Alpha-synuclein; Elongation factor 1 alpha; FASS; Lewy body dementia; Proteomics; Synapse.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Animals
  • Cerebral Cortex / metabolism
  • Cerebral Cortex / pathology
  • Computational Biology
  • Disease Models, Animal
  • Disks Large Homolog 4 Protein / metabolism
  • Female
  • Male
  • Mice, Transgenic
  • Neuropil / metabolism
  • Neuropil / pathology
  • Peptide Elongation Factor 1 / metabolism*
  • Proteome
  • Synapses / metabolism*
  • Synapses / pathology
  • Synucleinopathies / metabolism*
  • Synucleinopathies / pathology
  • alpha-Synuclein / genetics
  • alpha-Synuclein / metabolism

Substances

  • Disks Large Homolog 4 Protein
  • Dlg4 protein, mouse
  • EEF1A1 protein, human
  • Eef1a1 protein, mouse
  • Peptide Elongation Factor 1
  • Proteome
  • SNCA protein, human
  • alpha-Synuclein