Urine Steroid Metabolomics as a Novel Tool for Detection of Recurrent Adrenocortical Carcinoma

J Clin Endocrinol Metab. 2020 Mar 1;105(3):e307-e318. doi: 10.1210/clinem/dgz141.

Abstract

Context: Urine steroid metabolomics, combining mass spectrometry-based steroid profiling and machine learning, has been described as a novel diagnostic tool for detection of adrenocortical carcinoma (ACC).

Objective, design, setting: This proof-of-concept study evaluated the performance of urine steroid metabolomics as a tool for postoperative recurrence detection after microscopically complete (R0) resection of ACC.

Patients and methods: 135 patients from 14 clinical centers provided postoperative urine samples, which were analyzed by gas chromatography-mass spectrometry. We assessed the utility of these urine steroid profiles in detecting ACC recurrence, either when interpreted by expert clinicians or when analyzed by random forest, a machine learning-based classifier. Radiological recurrence detection served as the reference standard.

Results: Imaging detected recurrent disease in 42 of 135 patients; 32 had provided pre- and post-recurrence urine samples. 39 patients remained disease-free for ≥3 years. The urine "steroid fingerprint" at recurrence resembled that observed before R0 resection in the majority of cases. Review of longitudinally collected urine steroid profiles by 3 blinded experts detected recurrence by the time of radiological diagnosis in 50% to 72% of cases, improving to 69% to 92%, if a preoperative urine steroid result was available. Recurrence detection by steroid profiling preceded detection by imaging by more than 2 months in 22% to 39% of patients. Specificities varied considerably, ranging from 61% to 97%. The computational classifier detected ACC recurrence with superior accuracy (sensitivity = specificity = 81%).

Conclusion: Urine steroid metabolomics is a promising tool for postoperative recurrence detection in ACC; availability of a preoperative urine considerably improves the ability to detect ACC recurrence.

Keywords: ACC; adrenocortical carcinoma; machine learning; mass spectrometry; recurrence detection; steroid metabolomics.

Publication types

  • Evaluation Study
  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adrenal Cortex / diagnostic imaging
  • Adrenal Cortex / surgery
  • Adrenal Cortex Neoplasms / diagnosis*
  • Adrenal Cortex Neoplasms / surgery
  • Adrenal Cortex Neoplasms / urine
  • Adrenalectomy
  • Adrenocortical Carcinoma / diagnosis*
  • Adrenocortical Carcinoma / surgery
  • Adrenocortical Carcinoma / urine
  • Adult
  • Aged
  • Aged, 80 and over
  • Biomarkers, Tumor / urine*
  • Female
  • Follow-Up Studies
  • Gas Chromatography-Mass Spectrometry
  • Humans
  • Longitudinal Studies
  • Machine Learning
  • Male
  • Metabolomics / methods
  • Middle Aged
  • Neoplasm Recurrence, Local / diagnosis*
  • Neoplasm Recurrence, Local / prevention & control
  • Neoplasm Recurrence, Local / urine
  • Postoperative Period
  • Proof of Concept Study
  • Retrospective Studies
  • Sensitivity and Specificity
  • Steroids / urine*
  • Tomography, X-Ray Computed
  • Young Adult

Substances

  • Biomarkers, Tumor
  • Steroids