Acute Orbital Compromise after Intra-Arterial Chemotherapy in a Complex Retinoblastoma Associated with 13q Deletion Syndrome

Pediatr Neurosurg. 2020;55(5):295-298. doi: 10.1159/000511019. Epub 2020 Nov 11.

Abstract

Introduction: The intra-arterial chemotherapy (IAC) is increasingly used as a first-line therapy for retinoblastoma. The IAC has proved to be relatively safe. However, many local side effects of IAC have been described.

Case presentation: This case report describes a local side effect presenting as proptosis and myositis with vascular access difficulty of the middle meningeal artery, in a 2-year-old male with left eye diffuse multifocal stage Vb retinoblastoma complicated with retinal detachment.

Discussion/conclusion: IAC is assured to provide as efficient results in eliminating the tumor as the systemic chemotherapy, without causing the systemic side effects. It has become an alternative to systemic chemotherapy. A better understanding of the local side effects is required.

Keywords: 13q deletion syndrome; Intra-arterial chemotherapy; Local complication; Retinoblastoma.

Publication types

  • Case Reports

MeSH terms

  • Antineoplastic Combined Chemotherapy Protocols / administration & dosage
  • Antineoplastic Combined Chemotherapy Protocols / adverse effects*
  • Child, Preschool
  • Chromosome Deletion
  • Chromosome Disorders / complications
  • Chromosome Disorders / diagnostic imaging
  • Chromosome Disorders / drug therapy*
  • Chromosomes, Human, Pair 13
  • Exophthalmos / chemically induced
  • Exophthalmos / diagnostic imaging
  • Humans
  • Injections, Intra-Arterial / adverse effects*
  • Injections, Intra-Arterial / methods
  • Intravitreal Injections / methods
  • Male
  • Meningeal Arteries / diagnostic imaging
  • Meningeal Arteries / drug effects
  • Myositis / chemically induced
  • Myositis / diagnostic imaging
  • Orbital Diseases / chemically induced*
  • Orbital Diseases / diagnostic imaging
  • Retinal Neoplasms / complications
  • Retinal Neoplasms / diagnostic imaging
  • Retinal Neoplasms / drug therapy*
  • Retinoblastoma / complications
  • Retinoblastoma / diagnostic imaging
  • Retinoblastoma / drug therapy*

Supplementary concepts

  • 13q deletion syndrome