Mycosis fungoides and Sézary syndrome: Australian clinical practice statement

Australas J Dermatol. 2021 Feb;62(1):e8-e18. doi: 10.1111/ajd.13467. Epub 2020 Dec 26.

Abstract

Primary cutaneous lymphomas represent a heterogeneous group of T- and B-cell lymphomas with distinct clinical presentations, histopathologic features, treatment approaches and outcomes. The cutaneous T-cell lymphomas, which include mycosis fungoides and Sézary syndrome, account for the majority of the cutaneous lymphomas. This Clinical Practice Statement is reflective of the current clinical practice in Australia. An expanded form of the Clinical Practice Statement (and updates), along with helpful patient resources and access to support groups, can be found at the following (http://www.australasianlymphomaalliance.org.au).

Keywords: Sézary syndrome; clinical practices statement; cutaneous T-cell lymphoma; management; mycosis fungoides.

Publication types

  • Review

MeSH terms

  • Biopsy
  • Hematologic Tests
  • Humans
  • Mycosis Fungoides / diagnosis*
  • Mycosis Fungoides / mortality
  • Mycosis Fungoides / therapy*
  • Neoplasm Staging
  • Prognosis
  • Sezary Syndrome / diagnosis*
  • Sezary Syndrome / mortality
  • Sezary Syndrome / therapy*
  • Skin / pathology
  • Skin Neoplasms / diagnosis*
  • Skin Neoplasms / mortality
  • Skin Neoplasms / therapy*
  • Survival Rate