Repair of DNA Double-Strand Breaks by the Nonhomologous End Joining Pathway

Annu Rev Biochem. 2021 Jun 20:90:137-164. doi: 10.1146/annurev-biochem-080320-110356. Epub 2021 Feb 8.

Abstract

DNA double-strand breaks pose a serious threat to genome stability. In vertebrates, these breaks are predominantly repaired by nonhomologous end joining (NHEJ), which pairs DNA ends in a multiprotein synaptic complex to promote their direct ligation. NHEJ is a highly versatile pathway that uses an array of processing enzymes to modify damaged DNA ends and enable their ligation. The mechanisms of end synapsis and end processing have important implications for genome stability. Rapid and stable synapsis is necessary to limit chromosome translocations that result from the mispairing of DNA ends. Furthermore, end processing must be tightly regulated to minimize mutations at the break site. Here, we review our current mechanistic understanding of vertebrate NHEJ, with a particular focus on end synapsis and processing.

Keywords: DNA double-strand break; DNA end processing; DNA end synapsis; DNA repair; nonhomologous end joining.

Publication types

  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't
  • Review

MeSH terms

  • Animals
  • DNA Breaks, Double-Stranded*
  • DNA End-Joining Repair / physiology*
  • Enzymes / genetics
  • Enzymes / metabolism*
  • Genomic Instability
  • Humans
  • Models, Biological
  • Multiprotein Complexes / genetics*
  • Multiprotein Complexes / metabolism
  • V(D)J Recombination

Substances

  • Enzymes
  • Multiprotein Complexes