Subcutaneous immunoglobulin dose titration to clinical response in inflammatory neuropathy

J Neurol. 2021 Apr;268(4):1485-1490. doi: 10.1007/s00415-020-10318-3. Epub 2021 Feb 20.

Abstract

Introduction: Individualized dosing is an established approach in intravenous immunoglobulin (IVIg) treatment for inflammatory neuropathies. There is less experience in effective dosing strategies for subcutaneous (SC) immunoglobulin.

Methods: We conducted a retrospective cohort study of patients with inflammatory neuropathies transferring from IVIg to SCIg in two UK peripheral nerve services. I-RODS and grip strength were used to measure outcome. Dose and clinical progress were documented at 1 year and at last review.

Results: 44/56 patients remained on maintenance SCIg beyond 1 year (mean 3.3 years, range 1-9 years) with stable clinical outcomes. Clinical deteriorations were corrected by small increases in SCIg dose in 20 patients at 1 year, a further 9 requiring subsequent further up-titrations. Sixteen tolerated dose reduction. Mean dose change was + 2.4% from baseline. Two patients required IVIg bolus rescue (2 g/kg). Three patients successfully discontinued Ig therapy. Nine patients returned to IVIg due to clinical relapse or patient preference. Overall tolerance was good.

Discussion: Dose titration to clinical response is an effective approach in SCIg maintenance therapy.

Keywords: Chronic inflammatory demyelinating polyradiculoneuropathy; Immunoglobulin; Immunology; Peripheral neuropathy; Subcutaneous.

MeSH terms

  • Humans
  • Immunoglobulins, Intravenous / therapeutic use
  • Infusions, Intravenous
  • Infusions, Subcutaneous
  • Injections, Subcutaneous
  • Neuritis*
  • Polyradiculoneuropathy, Chronic Inflammatory Demyelinating* / drug therapy
  • Retrospective Studies

Substances

  • Immunoglobulins, Intravenous