Secondary AML Emerging After Therapy with Hypomethylating Agents: Outcomes, Prognostic Factors, and Treatment Options

Curr Hematol Malig Rep. 2021 Feb;16(1):97-111. doi: 10.1007/s11899-021-00608-6. Epub 2021 Feb 20.

Abstract

Purpose of review: Secondary AML (s-AML) encompasses a distinct subgroup of AML with either therapy-related AML or AML arising from preexisting myeloid neoplasms. Despite recent advances in the treatment armamentarium of AML, outcomes remain poor in s-AML. The purpose of this review is to highlight distinct characteristics, prognostic factors, and treatment options for patients with s-AML. Further, we focus on a distinctly poor-risk subgroup of s-AML with previous exposure to hypomethylating agents (HMAs) and describe ongoing clinical trials in this patient population.

Recent findings: CPX-351 (liposomal daunorubicin and cytarabine) is the first drug approved for s-AML and represents an advancement in the management of fit patients with this subtype of AML. Despite incremental improvement in remission rates and survival, long-term survival remains poor. Patients who have received prior HMAs for antecedent MDS rarely benefit from CPX-351 or other cytotoxic chemotherapy regimens. The approval of venetoclax in combination with azacitidine has led to a paradigm shift in the management of newly diagnosed older unfit AML patients; however, patients with s-AML and prior HMA therapy were excluded from the landmark randomized phase 3 study. Several early phase clinical trials with both low- and high-intensity therapies are ongoing for s-AML patients, though prior HMA exposure limits inclusion in many of these studies that include HMAs. Patients with s-AML previously treated with an HMA have dismal outcomes with standard therapeutic options and are under-represented in clinical trials. Trials investigating novel therapeutic options in this population are critically needed.

Trial registration: ClinicalTrials.gov NCT03289910.

Keywords: Acute myeloid leukemia; CPX-351; Clinical trials; Hypomethylating agents; Secondary AML; Venetoclax.

Publication types

  • Review

MeSH terms

  • Animals
  • Antineoplastic Agents / therapeutic use
  • Azacitidine / therapeutic use
  • Benzimidazoles / therapeutic use
  • Bridged Bicyclo Compounds, Heterocyclic / therapeutic use
  • Cytarabine / therapeutic use
  • Daunorubicin / therapeutic use
  • Gemtuzumab / therapeutic use
  • Humans
  • Induction Chemotherapy / methods
  • Leukemia, Myeloid, Acute / diagnosis
  • Leukemia, Myeloid, Acute / drug therapy*
  • Leukemia, Myeloid, Acute / etiology*
  • Leukemia, Myeloid, Acute / pathology
  • Molecular Targeted Therapy
  • Phenylurea Compounds / therapeutic use
  • Prognosis
  • Sulfonamides / therapeutic use

Substances

  • Antineoplastic Agents
  • Benzimidazoles
  • Bridged Bicyclo Compounds, Heterocyclic
  • CPX-351
  • Phenylurea Compounds
  • Sulfonamides
  • Cytarabine
  • Gemtuzumab
  • glasdegib
  • Azacitidine
  • venetoclax
  • Daunorubicin

Associated data

  • ClinicalTrials.gov/NCT03289910