Styloidogenic Jugular Venous Compression Syndrome with Papilloedema: Case Report and Review of the Literature

Neuroophthalmology. 2021 May 3;46(1):54-58. doi: 10.1080/01658107.2021.1887288. eCollection 2022.

Abstract

Styloidogenic jugular venous compression syndrome has been recently described as a new cause of idiopathic intracranial hypertension. We present a 69-year-old patient, without other relevant medical history, presenting with 3 years of positional headache associated with decreased vision when reading and while turning her head to the right or left. She also reported pulsatile low-frequency tinnitus. Papilloedema was noted on the physical examination and, on imaging, an enlarged styloid process that induced jugular vein compression. The patient underwent styloidectomy with resolution of her symptoms and normalisation of her visual fields.

Keywords: Papilloedema; eagle syndrome; intracranial hypertension; jugular venous compression; styloid process.

Publication types

  • Case Reports

Grants and funding

This work was partially supported by the Pan-American Ophthalmological Foundation (PAOO) and the Retina Research Foundation (RRF) (2019 Gillingham Grant). The funding bodies did not have any role in the design of the study and collection, analysis, and interpretation of data and in writing the manuscript.