PTPRD and DCC Are Novel BACE1 Substrates Differentially Expressed in Alzheimer's Disease: A Data Mining and Bioinformatics Study

Int J Mol Sci. 2022 Apr 20;23(9):4568. doi: 10.3390/ijms23094568.

Abstract

The β-site Amyloid precursor protein Cleaving Enzyme 1 (BACE1) is an extensively studied therapeutic target for Alzheimer's disease (AD), owing to its role in the production of neurotoxic amyloid beta (Aβ) peptides. However, despite numerous BACE1 inhibitors entering clinical trials, none have successfully improved AD pathogenesis, despite effectively lowering Aβ concentrations. This can, in part, be attributed to an incomplete understanding of BACE1, including its physiological functions and substrate specificity. We propose that BACE1 has additional important physiological functions, mediated through substrates still to be identified. Thus, to address this, we computationally analysed a list of 533 BACE1 dependent proteins, identified from the literature, for potential BACE1 substrates, and compared them against proteins differentially expressed in AD. We identified 15 novel BACE1 substrates that were specifically altered in AD. To confirm our analysis, we validated Protein tyrosine phosphatase receptor type D (PTPRD) and Netrin receptor DCC (DCC) using Western blotting. These findings shed light on the BACE1 inhibitor failings and could enable the design of substrate-specific inhibitors to target alternative BACE1 substrates. Furthermore, it gives us a greater understanding of the roles of BACE1 and its dysfunction in AD.

Keywords: Alzheimer’s disease; BACE1 substrates; Netrin receptor DCC; beta secretase 1 (BACE1); protein tyrosine phosphatase receptor type D (PTPRD).

MeSH terms

  • Alzheimer Disease* / genetics
  • Alzheimer Disease* / metabolism
  • Amyloid Precursor Protein Secretases / genetics
  • Amyloid Precursor Protein Secretases / metabolism
  • Amyloid beta-Peptides / genetics
  • Amyloid beta-Peptides / metabolism
  • Amyloid beta-Protein Precursor / genetics
  • Amyloid beta-Protein Precursor / metabolism
  • Aspartic Acid Endopeptidases / metabolism
  • Computational Biology
  • DCC Receptor* / genetics
  • DCC Receptor* / metabolism
  • Data Mining
  • Humans
  • Phosphoric Monoester Hydrolases
  • Receptor-Like Protein Tyrosine Phosphatases, Class 2* / genetics
  • Receptor-Like Protein Tyrosine Phosphatases, Class 2* / metabolism

Substances

  • Amyloid beta-Peptides
  • Amyloid beta-Protein Precursor
  • DCC Receptor
  • DCC protein, human
  • Phosphoric Monoester Hydrolases
  • PTPRD protein, human
  • Receptor-Like Protein Tyrosine Phosphatases, Class 2
  • Amyloid Precursor Protein Secretases
  • Aspartic Acid Endopeptidases
  • BACE1 protein, human