JAK/STAT blockade reverses the malignant phenotype of Hodgkin and Reed-Sternberg cells

Blood Adv. 2023 Aug 8;7(15):4135-4147. doi: 10.1182/bloodadvances.2021006336.

Abstract

Constitutive activation of the JAK/STAT pathway is a common phenomenon in classic Hodgkin lymphoma (cHL). The clinical potential of anti-JAK/STAT therapy is being explored in early-stage clinical trials. Notwithstanding, very little information is available about the complex biological consequences of this blockade. Here, we investigated the effects of JAK/STAT pharmacological inhibition on cHL cell models using ruxolitinib, a JAK 1/2 inhibitor that induces apoptosis by concentration- and time-dependent mechanisms. An unbiased whole-transcriptome approach identified expression of the anti-GCSF receptor (CSF3R) as a potential surrogate biomarker of JAK/STAT overactivation. In addition, longitudinal gene expression analyses provided further mechanistic information about pertinent biological pathways involved, including 37 gene pathways distributed in 3 main clusters: cluster 1 was characterized by upregulation of the G2/M checkpoint and major histocompatibility complex-related clusters; 2 additional clusters (2 and 3) showed a progressive downregulation of the tumor-promoting inflammation signatures: JAK/STAT and interleukin 1 (IL-1)/IL-4/IL-13/IL-17. Together, our results confirm the therapeutic potential of JAK/STAT inhibitors in cHL, identify CSF3R as a new biomarker, and provide supporting genetic data and mechanistic understanding.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Hodgkin Disease* / genetics
  • Humans
  • Janus Kinases
  • Phenotype
  • Reed-Sternberg Cells*
  • STAT Transcription Factors / metabolism
  • Signal Transduction

Substances

  • Janus Kinases
  • STAT Transcription Factors