Bilateral Macular Holes in Adult Vitelliform Macular Dystrophy

J Vitreoretin Dis. 2020 Feb 10;4(4):340-343. doi: 10.1177/2474126420903544. eCollection 2020 Jul-Aug.

Abstract

Purpose: This report describes a case of bilateral macular holes (MHs) in adult vitelliform macular dystrophy (AVMD).

Methods: A retrospective case report of a patient with AVMD and sequential onset of bilateral MHs is presented.

Results: Bilateral MHs were observed after vitreomacular traction was identified on optical coherence tomography. Holes in both eyes were repaired with pars plana vitrectomy (PPV) with C3F8 (perfluoropropane) gas tamponade; only the right eye underwent internal limiting membrane peeling. In the right eye, 2 PPVs were required for hole closure. In both eyes, long-term atrophy of the retina and retinal pigment epithelium was observed.

Conclusions: MHs in AVMD may be preceded by vitreomacular traction. Surgical repair with PPV and gas tamponade was successful. Retinal and retinal pigment epithelium atrophy developed postoperatively, but the patient's vision still improved.

Keywords: adult vitelliform macular dystrophy; internal limiting membrane peel; macular hole; vitreomacular traction.

Publication types

  • Case Reports