Diffuse pulmonary meningotheliomatosis

Respirol Case Rep. 2023 Jun 21;11(7):e01183. doi: 10.1002/rcr2.1183. eCollection 2023 Jul.

Abstract

Diffuse pulmonary meningotheliomatosis (DPM) is an ultra-rare pulmonary disease characterized by innumerable bilateral minute meningothelial-like nodules, sometimes presenting a characteristic 'cheerio-sign' on imaging. Most patients with DPM are asymptomatic and experience no disease progression. Although little is known about its nature, DPM may be associated with pulmonary malignancies, mostly lung adenocarcinoma.

Keywords: chest computed tomography; pulmonary meningotheliomatosis; pulmonary nodule.