Epilepsy and nodding syndrome in association with an Onchocerca volvulus infection drive distinct immune profile patterns

PLoS Negl Trop Dis. 2023 Aug 3;17(8):e0011503. doi: 10.1371/journal.pntd.0011503. eCollection 2023 Aug.

Abstract

Previous studies have described the association of onchocerciasis (caused by Onchocerca volvulus) with epilepsy, including nodding syndrome, although a clear etiological link is still missing. Cases are found in different African countries (Tanzania, South Sudan, Uganda, Democratic Republic of the Congo, Central African Republic and Cameroon). In our study we investigated immunological parameters (cytokine, chemokine, immunoglobulin levels) in individuals from the Mahenge area, Tanzania, presenting with either epilepsy or nodding syndrome with or without O. volvulus infection and compared them to O. volvulus negative individuals from the same endemic area lacking neurological disorders. Additionally, cell differentiation was performed using blood smears and systemic levels of neurodegeneration markers, leiomodin-1 and N-acetyltyramine-O, β-glucuronide (NATOG) were determined. Our findings revealed that cytokines, most chemokines and neurodegeneration markers were comparable between both groups presenting with epilepsy or nodding syndrome. However, we observed elevated eosinophil percentages within the O. volvulus positive epilepsy/nodding syndrome patients accompanied with increased eosinophilic cationic protein (ECP) and antigen-specific IgG levels in comparison to those without an O. volvulus infection. Furthermore, highest levels of NATOG were found in O. volvulus positive nodding syndrome patients. These findings highlight that the detection of distinct biomarkers might be useful for a differential diagnosis of epilepsy and nodding syndrome in O. volvulus endemic areas. Trial-registration: NCT03653975.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Animals
  • Cytokines
  • Epilepsy* / epidemiology
  • Humans
  • Intestinal Volvulus* / complications
  • Nodding Syndrome* / epidemiology
  • Nodding Syndrome* / etiology
  • Onchocerca volvulus*
  • Onchocerciasis* / epidemiology
  • Uganda / epidemiology

Substances

  • Cytokines

Associated data

  • ClinicalTrials.gov/NCT03653975

Grants and funding

JK was funded by the Deutsche Gesellschaft für Epileptologie (DGFE). The clinical leave stipend of TW was supported by a grant from the German Center of Infectious Disease (DZIF; Verbundprojekt: TI 07.001) of which ASW, CP and AH were co-applicants. In addition, AH, CP, KP and LEL are members of DZIF. AH is supported by the BMBF [01KA1611, 01KA2027 and 01KA2113A] and additionally funded by the Deutsche Forschungsgemeinschaft (DFG) under Germany’s Excellence Strategy – EXC2151 – 390873048. DM received financial support from the DFG [Project-ID 398967434 – TRR 261. The funders had no role in study design, data collection and analysis, decision to publish, or preparation of the manuscript.