Pulmonary ceroidosis

Chest. 1987 Feb;91(2):281-3. doi: 10.1378/chest.91.2.281.

Abstract

We describe a patient with pulmonary ceroid histiocytosis. Skin pigmentation, chest x-ray film and laboratory findings were normal. Only pulmonary function tests were abnormal (TLC = 63 percent, DLco = 52 percent). Based on these functional data, the patient was submitted to a lung biopsy by thoracotomy. Brown pigmented histiocytes were shown occupying alveolar spaces. Similar brown pigmented hepatocytes were seen in the liver biopsy.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Bone Marrow / metabolism
  • Ceroid / metabolism*
  • Female
  • Follow-Up Studies
  • Histiocytes / metabolism
  • Histocytochemistry
  • Humans
  • Liver / metabolism
  • Lung Neoplasms / drug therapy
  • Lung Neoplasms / metabolism*
  • Lung Neoplasms / pathology
  • Lymphatic Diseases / drug therapy
  • Lymphatic Diseases / metabolism*
  • Lymphatic Diseases / pathology
  • Pigments, Biological / metabolism*
  • Respiratory Function Tests

Substances

  • Ceroid
  • Pigments, Biological