Body composition in children with cystic fibrosis treated with CFTR modulators versus modulator naïve individuals

Pediatr Pulmonol. 2024 Mar;59(3):805-808. doi: 10.1002/ppul.26797. Epub 2023 Dec 20.

Authors

Carolyn Dress¹, Elizabeth Hente¹, Md M Hossain^{1

2

3}, William Hardie^{1

2}, Michelle Hjelm^{1

2}, Thomas Boat^{1

2}

Affiliations

¹ Division of Pulmonary Medicine , Cincinnati Children's Hospital Medical Center, Cincinnati, Ohio, USA.
² Department of Pediatrics, University of Cincinnati College of Medicine, Cincinnati, Ohio, USA.
³ Division of Biostatistics and Epidemiology, Cincinnati Children's Hospital Medical Center, Cincinnati, Ohio, USA.

PMID: 38116856
DOI: 10.1002/ppul.26797

No abstract available

Keywords: BMI; body composition; children with CF; modulator therapy.

Publication types

Letter

MeSH terms

Aminophenols / therapeutic use
Aminopyridines / therapeutic use
Body Composition
Child
Cystic Fibrosis Transmembrane Conductance Regulator / genetics
Cystic Fibrosis Transmembrane Conductance Regulator / metabolism
Cystic Fibrosis* / drug therapy
Cystic Fibrosis* / genetics
Humans
Mutation

Substances

Cystic Fibrosis Transmembrane Conductance Regulator
Aminophenols
Aminopyridines
CFTR protein, human

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