[Acute myeloid leukemia with type I CBFB::MYH11 fusion gene not detected by screening test for leukemia-related chimeric genes]

Rinsho Ketsueki. 2023;64(12):1503-1507. doi: 10.11406/rinketsu.64.1503.
[Article in Japanese]

Abstract

A 27-year-old woman with pancytopenia was admitted to our hospital. Bone marrow aspiration revealed 52.2% myeloperoxidase-positive myeloblasts, leading to a diagnosis of acute myeloid leukemia. While a screening test for chimeric genes related to leukemia initially yielded negative results, including for the CBFB::MYH11 fusion gene, G-banded karyotyping uncovered the presence of inv (16)(p13.1q22). Further investigation by fluorescence in situ hybridization (FISH) confirmed the split signals for CBFB. A second screening test for leukemia-related chimeric genes with different PCR primers revealed the elusive CBFB::MYH11 fusion gene. Subsequently, the type I CBFB::MYH11 fusion gene was identified through exhaustive exploration using RNA sequencing for fusion gene discovery. This exceptional case highlights the existence of a distinctive subtype of CBFB::MYH11 that may yield false-negative results in conventional chimeric fusion screening, thus emphasizing the indispensable utility of PCR primer modification, FISH, and RNA sequencing in the investigative process.

Keywords: Screening test for leukemia-related chimeric genes; Type I CBFB::MYH11; inv (16)(p13.1q22).

Publication types

  • Case Reports
  • English Abstract

MeSH terms

  • Adult
  • Core Binding Factor beta Subunit / genetics
  • Female
  • Humans
  • In Situ Hybridization, Fluorescence
  • Karyotyping
  • Leukemia, Myeloid, Acute* / diagnosis
  • Leukemia, Myeloid, Acute* / genetics
  • Myosin Heavy Chains / genetics
  • Oncogene Proteins, Fusion / genetics

Substances

  • Oncogene Proteins, Fusion
  • CBFB protein, human
  • Core Binding Factor beta Subunit
  • MYH11 protein, human
  • Myosin Heavy Chains