Ebstein's anomaly: an electrophysiological perspective

Anunay Gupta; Mukund A Prabhu; Robert D Anderson; Srinivas Bv Prasad; Timothy Campbell; Samual Turnbull; Geoffrey Lee; Jonathan R Skinner; Jonathan Kalman; Saurabh Kumar

doi:10.1007/s10840-024-01744-8

Ebstein's anomaly: an electrophysiological perspective

J Interv Card Electrophysiol. 2024 Jun;67(4):887-900. doi: 10.1007/s10840-024-01744-8. Epub 2024 Jan 30.

Authors

Affiliations

¹ Department of Cardiology, Westmead Hospital, Westmead Applied Research Centre, University of Sydney, Darcy Road, Westmead, Sydney, New South Wales, 2145, Australia.
² Department of Cardiology, Vardhman Mahavir Medical College and Safdarjung Hospital, New Delhi, India.
³ Department of Cardiology, Kasturba Medical College Manipal, Manipal Academy of Higher Education, Manipal, Karnataka, India.
⁴ Department of Cardiology, Royal Melbourne Hospital, University of Melbourne, Parkville, Victoria, Australia.
⁵ Department of Cardiology, Fortis Hospital, Bannerghatta, Bengaluru, India.
⁶ Department of Cardiology, Children's Hospital Westmead, Westmead, New South Wales, Australia.
⁷ Department of Cardiology, Westmead Hospital, Westmead Applied Research Centre, University of Sydney, Darcy Road, Westmead, Sydney, New South Wales, 2145, Australia. saurabh.kumar@sydney.edu.au.

Abstract

Ebstein's anomaly of the tricuspid valve (EA) is an uncommon congenital cardiac malformation. It can present with atrioventricular tachycardia (AVRT), atrioventricular nodal re-entrant tachycardia (AVNRT), atrial arrhythmias, and rarely with ventricular tachycardia. The 12-lead electrocardiogram (ECG) is critically important and often diagnostic even prior to an electrophysiology study (EPS). Due to its complex anatomy, it poses particular challenges for mapping and ablation, even for an experienced electrophysiologist. In this review, we aim to provide insight into the electrophysiological perspective of EA and an in-depth analysis of the various arrhythmias encountered in diverse clinical scenarios.

Keywords: Ablation; Arrhythmia; Ebstein anomaly.

Publication types

Review

MeSH terms

Catheter Ablation / methods
Ebstein Anomaly* / diagnostic imaging
Ebstein Anomaly* / physiopathology
Ebstein Anomaly* / surgery
Electrocardiography* / methods
Electrophysiologic Techniques, Cardiac / methods
Female
Humans
Male
Tachycardia, Atrioventricular Nodal Reentry / diagnosis
Tachycardia, Atrioventricular Nodal Reentry / physiopathology
Tachycardia, Atrioventricular Nodal Reentry / surgery