PLK1-mediated phosphorylation cascade activates Mis18 complex to ensure centromere inheritance

Science. 2024 Sep 6;385(6713):1098-1104. doi: 10.1126/science.ado8270. Epub 2024 Sep 5.

Abstract

Accurate chromosome segregation requires the attachment of microtubules to centromeres, epigenetically defined by the enrichment of CENP-A nucleosomes. During DNA replication, CENP-A nucleosomes undergo dilution. To preserve centromere identity, correct amounts of CENP-A must be restored in a cell cycle-controlled manner orchestrated by the Mis18 complex (Mis18α-Mis18β-Mis18BP1). We demonstrate here that PLK1 interacts with the Mis18 complex by recognizing self-primed phosphorylations of Mis18α (Ser54) and Mis18BP1 (Thr78 and Ser93) through its Polo-box domain. Disrupting these phosphorylations perturbed both centromere recruitment of the CENP-A chaperone HJURP and new CENP-A loading. Biochemical and functional analyses showed that phosphorylation of Mis18α and PLK1 binding were required to activate Mis18α-Mis18β and promote Mis18 complex-HJURP interaction. Thus, our study reveals key molecular events underpinning the licensing role of PLK1 in ensuring accurate centromere inheritance.

MeSH terms

  • Adaptor Proteins, Signal Transducing* / metabolism
  • Cell Cycle Proteins* / metabolism
  • Centromere Protein A* / metabolism
  • Centromere* / metabolism
  • Chromosomal Proteins, Non-Histone* / metabolism
  • Chromosome Segregation
  • DNA-Binding Proteins / metabolism
  • HeLa Cells
  • Humans
  • Phosphorylation
  • Polo-Like Kinase 1*
  • Protein Serine-Threonine Kinases* / metabolism
  • Proto-Oncogene Proteins* / genetics
  • Proto-Oncogene Proteins* / metabolism

Substances

  • Cell Cycle Proteins
  • CENPA protein, human
  • Centromere Protein A
  • Chromosomal Proteins, Non-Histone
  • DNA-Binding Proteins
  • HJURP protein, human
  • Polo-Like Kinase 1
  • Protein Serine-Threonine Kinases
  • Proto-Oncogene Proteins
  • MIS18A protein, human
  • Adaptor Proteins, Signal Transducing
  • MIS18BP1 protein, human